The Autosomal Recessive Inheritance of Hereditary Gingival Fibromatosis
نویسندگان
چکیده
Hereditary gingival fibromatosis (HGF) is a rare condition which is marked by enlargement of gingival tissue that covers teeth to various extents leading to aesthetic disfigurement. This study presents a case of a 28-year-old female patient and 18-year-old male who belong to the same family suffering from HGF with chief complaint of overgrowing swelling gingiva. The presence of enlarged gingiva with the same eruption was found in their other family members with no concomitant drug or medical history, and the occurrence of HGF has been found in one generation of this family which may indicate the autosomal recessive inheritance pattern of HGF. Hereditary gingival fibromatosis is an idiopathic condition as its etiology is unknown and it was found to recur in some cases even after surgical treatment. Both patients underwent thorough oral prophylaxis and later surgical therapy to correct the deformity.
منابع مشابه
Juvenile hyaline fibromatosis.
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Hereditary Gingival Fibromatosis (HGF) also referred to as idiopathic gingival hyperplasia is a rare type of slow growing gingival enlargement with great clinical and genetic heterogenity inherited usually as Mendelian autosomal dominant fashion. Occurring as an isolated trait (HGF) and/or as a component of a syndrome, the affected gingiva is characterized by firm, asymptomatic, nonhemorrhagic ...
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ورودعنوان ژورنال:
دوره 2013 شماره
صفحات -
تاریخ انتشار 2013